"I'm Ready" is a song by the South Korean singer and actress Sori featuring the rapper Jaehyun. The song was released on December 26, 2018. "I'm Ready" was arranged and penned by the record producer Gamen Rider. The music video premiered on December 22, 2018, four days prior to the release of the single, was directed by the film director Kyotaro Hayashi. Following the conclusion of the promotional activities for the Japanese version of "Touch", Sori launched a Kickstarter project on December 7, 2018 in order to fund her sophomore release titled "I'm Ready", she subsequently uploaded videos of herself preparing the rewards for the supporters of the project on her official YouTube channel, which included a custom-made baseball cap with the song title printed on the front panels. When the project concluded on December 21, 2018, the project raised more than ¥3,000,000 by 260 supporters. "I'm Ready" is an uptempo moombahton dance song with an "addictive refrain". The song is a musical departure from Sori's previous releases as a member of both CocoSori and Real Girls Project as well as "Touch", seeing her embrace a much more "mature" sound.
"I'm Ready" was arranged and penned by the record producer Gamen Rider, who produced Sori's aforementioned debut single. The song features the rapper Jaehyun. Following the re-release of the single on February 8, 2019 in Japan, "I'm Ready" enjoyed minor commercial success, where it debuted and peaked at number 126 on the Oricon Singles Chart on the chart issued on February 18, 2019. A teaser of the music video for "I'm Ready" was released on December 17, 2018, it premiered on December 21, 2018 following the conclusion of the Kickstarter project and four days prior to the release of the single through music portals. It was filmed in several locations: the interior and the rooftop of a warehouse in Yokohama, a bridge near the Yamanote Line and the rooftop of a building in Shinjuku. A choreography-centered video for the song premiered on January 5, 2019, filmed in the temperature -7ºC; the choreography was created by the choreographers MikuNana. The music video opens with a train passing behind Sori.
Subsequent scenes see her accompanied by MikuNana performing the choreography of "I'm Ready" in multiple settings including the interior of a warehouse, in front of shipping containers, on top of a rooftop, during which they are joined by numerous dancers for the final chorus. The video closes with Sori crossing a pedestrian crossing. Due to the single being released during the holiday season, Sori began promoting "I'm Ready" a month following its release, she performed the song on several music programs including SBS MTV's The Show. In addition to her music program performances, Sori held a street performance in Hongdae, where she was accompanied by the South Korean internet personality StarTy for a performance of "I'm Ready" as well as other songs including "Touch", "What Is Love?" by the girl group Twice, "Ddu-Du Ddu-Du" by the girl group Blackpink. The song was performed during her first Japanese fanmeet titled "SoriNation in Japan", held on February 11, 2019 at Club Citta in Kawasaki, Kanagawa
Pieces in a Modern Style 2 is the 11th album by British electronic musician and record producer, William Orbit. A follow-up to Orbit's 1995 album Pieces in a Modern Style, it was released in compact disc and digital download formats on 22 August 2010 through Decca Records. Orbit's second foray into classical music by way of electronic instrumentation includes, among others, a selection from Pyotr Ilyich Tchaikovsky's Swan Lake. A 2-CD version, with remixes and additional pieces was released. A Deutsche Grammophon 2010 release Classic Originals - Pieces In The Original Style 2 featured the original versions of the tracks on this CD, which included contributions from Cristina Ortiz, Pascal Rogé, András Schiff, Iona Brown and Renée Fleming.
IT energy management or Green IT as per International Federation of Global & Green ICT "IFGICT" is the analysis and management of energy demand within the Information Technology department in any organization. IT energy demand accounts for 2% of global CO2 emissions the same level as aviation, represents over 10% of all the global energy consumption. IT can account for 25% of a modern office building’s energy cost. At one point, the main sources of manageable IT energy demand were PCs and Monitors, accounting for 39% of energy use, followed by data centers and servers, accounting for 23% of energy use. In 2006, US IT infrastructures consumed an estimated 61 billion kWh of energy, totaling to a cost of $4.5 billion. Significant opportunities exist for Enterprises to optimise their IT energy usage. Computers, data centers and networks consume 10% of the world’s electricity. 30% of this electricity goes to power terminal equipment, 30% goes to data centers and 40% goes to the network. A router consumes 10 kW and a large data center consumes nearly 100MW.
Data centers can consume up to 100 times more energy than a standard office building. Less than 15% of original source energy is used for the information technology equipment within a data center. With the introduction of new technologies and products, energy management of several IT equipments has been improved. Servers and data centers account for 23% of IT energy demand; as hardware becomes smaller and less expensive, energy costs constitute a larger portion of server or data center costs. These allow gains to be made through optimisation of servers; this is done by doing diagnostic tests on individual servers and developing a model for a data center’s energy demand using these measurements. By analysing every server in a data centre, server power management software can identify servers that can be removed, it enables servers to be virtualized, processes to be consolidated to a smaller number of servers, servers with a predictable cyclical power demand to be powered down when not in use. Active power management features are included which put remaining servers into their lowest power state that allows instant wake-up on demand when required.
Energy efficiency benchmarks, such as SPECpower, or specifications, like Average CPU power, can be used for comparing server efficiency and performance per watt. A research study shows that in the US, 50% of PCs are left on overnight, resulting in an estimated annual energy waste of 28.8 billion kWh, a cost of $2.8 billion per year. User behaviour is different in Europe, with 28% of PCs being left on overnight in the UK, resulting in an estimated energy loss of 2.5 billion kWh, costing £300 million per year. In Germany, with 30% of PCs left on overnight, it is estimated 4.8 billion kWh of energy are wasted each year, costing €919 million There is a significant market in third-party Power Management Software offering features beyond those present in the Windows operating system. Most products offer Active Directory integration and per-user/per-machine settings with the more advanced offering multiple power plans, scheduled power plans, anti-insomnia features and enterprise power usage reporting.
Energy Efficient Ethernet could reduce the energy use of networking equipment. In 2005, all the network-interface controllers in the United States used an estimated 5.3 terawatt-hours of electricity. According to a researcher at the Lawrence Berkeley Laboratory, Energy Efficient Ethernet could save an estimated $450 million a year in energy costs in the U. S. With most of the savings from home computers, offices, the remaining $80 million from data centers. Energy efficient Ethernet saves energy by allowing network links to either go into a low power sleep mode or run at a slower rate when there is no data, it defines lower power signaling for use on higher quality cables. There are a number of industry associations and policy organisations whose work on promoting energy efficiency includes providing resources and information on IT energy management; these include: The Green Grid Alliance to Save Energy Climate Savers Computing Initiative 2Degrees Energy-Efficient Ethernet Performance per watt
Guus Til is a Zambian-born Dutch professional footballer who plays as a midfielder for Spartak Moscow. Til is a youth exponent from AZ, he made his professional debut on 4 August 2016 as a substitute in a UEFA Europa League play-off match against PAS Giannina, replacing Joris van Overeem after 71 minutes. On 5 August 2019, Spartak Moscow announced they had signed Guus Til from AZ for a reported transfer fee of €18 million, he signed a 4 year contract with the club. In his Russian Premier League debut on 11 August 2019 against FC Akhmat Grozny, he provided 2 assists in a 3–1 victory, he scored his first goal for Spartak on 25 August 2019 in an away game against PFC Krylia Sovetov Samara, when his added-time goal gave his team a 2–1 comeback away victory. Til is a youth international for the Netherlands. Til earned his first full international call up in Ronald Koeman’s first Dutch national football team squad in March 2018, he made his debut coming on as a subsistute in a 3–0 win against Portugal on 26 March 2018.
As of 25 July 2019 Guus Til at WorldFootball.net U21 profile at Ons Oranje U20 profile at Ons Oranje Profile at Voetbal International
In linguistics, phonology, stress or accent is relative emphasis or prominence given to a certain syllable in a word, or to a certain word in a phrase or sentence. That emphasis is caused by such properties as increased loudness and vowel length, full articulation of the vowel, changes in pitch; the terms stress and accent are used synonymously in that context but are sometimes distinguished. For example, when emphasis is produced through pitch alone, it is called pitch accent, when produced through length alone, it is called quantitative accent; when caused by a combination of various intensified properties, it is called stress accent or dynamic accent. Since stress can be realised through a wide range of phonetic properties, such as loudness, vowel length, pitch, which are used for other linguistic functions, it is difficult to define stress phonetically; the stress placed on syllables within words is called lexical stress. Some languages have fixed stress, meaning that the stress on any multisyllable word falls on a particular syllable, such as the penultimate or the first.
Other languages, like English and Russian, have variable stress, where the position of stress in a word is not predictable in that way. Sometimes more than one level of stress, such as primary stress and secondary stress, may be identified. However, some languages, such as French and Mandarin, are sometimes analyzed as lacking lexical stress entirely; the stress placed on words within sentences is called prosodic stress. That is one of the three components of prosody, along with intonation, it includes phrasal stress, contrastive stress. There are various ways in which stress manifests itself in the speech stream, these depend to some extent on which language is being spoken. Stressed syllables are louder than non-stressed syllables, may have a higher or lower pitch, they may sometimes be pronounced longer. There are sometimes differences in place or manner of articulation – in particular, vowels in unstressed syllables may have a more central articulation, while those in stressed syllables have a more peripheral articulation.
Stress may be realized to varying degrees on different words in a sentence. These particular distinguishing features of stress, or types of prominence in which particular features are dominant, are sometimes referred to as particular types of accent – dynamic accent in the case of loudness, pitch accent in the case of pitch, quantitative accent in the case of length, qualitative accent in the case of differences in articulation; these can be compared to the various types of accent in music theory. In some contexts, the term stress or stress accent is used to mean dynamic accent. A prominent syllable or word is said to be tonic. Other syllables or words are said to be atonic. Syllables are said to be in pretonic or post-tonic position. For instance, in American English, /t/ and /d/ are flapped in post-tonic position. In Mandarin Chinese, a tonal language, stressed syllables have been found to have tones realized with a large swing in fundamental frequency, while unstressed syllables have smaller swings.
Stressed syllables are perceived as being more forceful than non-stressed syllables. Lexical stress, or word stress, is the stress placed on a given syllable in a word; the position of lexical stress in a word may depend on certain general rules applicable in the language or dialect in question, but in other languages, it must be learned for each word, as it is unpredictable. In some cases, classes of words in a language differ in their stress properties. In some languages, the placement of stress can be determined by rules, it is thus not a phonemic property of the word, because it can always be predicted by applying the rules. Languages in which the position of the stress can be predicted by a simple rule are said to have fixed stress. For example, in Czech, Finnish and Hungarian, the stress always comes on the first syllable of a word. In Armenian the stress is on the last syllable of a word. In Quechua and Polish, the stress is always on the penult. In Macedonian, it is on the antepenult. Other languages have stress placed on different syllables but in a predictable way, as in Classical Arabic and Latin, where stress is conditioned by the structure of particular syllables.
They are said to have a regular stress rule. Statements about the position of stress are sometimes affected by the fact that when a word is spoken in isolation, prosodic factors come into play, which do not apply when the word is spoken within a sentence. French words are sometimes said to be stressed on the final syllable, but that can be attributed to the prosodic stress, placed on the last syllable of any string of words in that language. Thu
Kniest dysplasia is a rare form of dwarfism caused by a mutation in the COL2A1 gene on chromosome 12. The COL2A1 gene is responsible for producing type II collagen; the mutation of COL2A1 gene leads to problems with hearing and vision. What characterizes Kniest dysplasia from other type II osteochondrodysplasia is the level of severity and the dumb-bell shape of shortened long tubular bones; this condition was first diagnosed by Dr. Wilhelm Kniest in 1952. Dr. Kniest noticed that his 50-year-old patient was having difficulties with restricted joint mobility; the patient had a short stature and was suffering from blindness. Upon analysis of the patient's DNA, Dr. Kniest discovered that a mutation had occurred at a splice site of the COL2A1 gene; this condition is rare and occurs less than 1 in 1,000,000 people. Males and females have equal chances of having this condition. There is no cure for Kniest dysplasia. Alternative names for Kniest Dysplasia can include Kniest syndrome, swiss cheese cartilage syndrome, Kniest chondrodystrophy, or metatrophic dwarfism type II.
Because collagen plays an important role in the development of the body, people with Kniest Dysplasia will have their first symptoms at birth. These symptoms can include: Musculoskeletal Problems Short limbs Shortened body trunk Flattened bones in the spine kyphoscoliosis Scoliosis Early development of arthritis Respiratory problems Respiratory tract infection Difficulty breathing Eye problems Severe myopia Cataract Cranial structure may elongate the eyeball, causing a thinning of the retina, thereby predisposing retinal detachment Hearing problems progressive hearing loss ear infectionsMost symptoms are chronic and will continue to worsen as the individual ages, it is essential to have regular checkups with general doctors, ophthalmologists, and/or otorhinolaryngologists. This will help to detect. Studies have shown that a mutated COL2A1 gene is responsible for all type II chondroldysplasias, including Kniest dysplasia, it is believed that point mutations or the alteration of splice sites in COL2A1 domains will result in Kniest Dysplasia.
The COL2A1 domain spans between exon 12 and 24. Mutations that occur at a splice donor site results in the loss of function at that site; this leads to the skipping of the deletion of amino acids. The loss of these amino acids result in an abnormal procollagen II structure; the structure is not stable like the normal procollagen II structure and is degraded at a faster rate. Kniest dysplasia is an autosomal dominant condition; this means that the person only needs to have one copy of the mutated gene in order to have the condition. People with a family history are at a higher risk of having the disease than people with no family history. A random mutation in the gene can cause a person with no family history to have the condition. A combination of medical tests are used to diagnosis Kniest dysplasia; these tests can include: Computer Tomography Scan - This test uses multiple images taken at different angles to produce a cross-sectional image of the body. Magnetic Resonance Imaging - This technique proves detailed images of the body by using magnetic fields and radio waves.
EOS Imaging - EOS imaging provides information on how musculoskeletal system interacts with the joints. The 3D image is scanned while the patient is standing and allows the physician to view the natural, weight-bearing posture. X-rays - X-ray images will allow the physician to have a closer look on whether or not the bones are growing abnormally; the images taken will help to identify any bone anomalies. Two key features to look for in a patient with Kniest dysplasia is the presence of dumb-bell shaped femur bones and coronal clefts in the vertebrae. Other features to look for include: Platyspondyly Kyphoscoliosis Abnormal growth of epiphyses and diaphysis Short tubular bones Narrowed joint spacesGenetic Testing - A genetic sample may be taken in order to look at the patient's DNA. Finding an error in the COL2A1 gene will help identify the condition as a type II chondroldysplasia; because Kniest dysplasia can affect various body systems, treatments can vary between non-surgical and surgical treatment.
Patients will be monitored over time, treatments will be provided based on the complications that arise. Spinal Fusion for patients with severe kyphoscoliosis Extension Osteotomy to help treat progressive joint limitation Surgical realignment Retinal Detachment repair Myringotomy Routine monitoring Oxygen support, CPAP, Mechanical Ventilation Physical therapy BracingLike treatment options, the prognosis is dependent on the severity of the symptoms. Despite the various symptoms and limitations, most individuals have normal intelligence and can lead a normal life. A recent article in 2015 reported a persistent notochord in a fetus at 23 weeks of gestation; the fetus had shortened long bones and a left clubfoot. After running postmortem tests and ultrasound, the researchers believed that the fetus suffered from hypochondrogenesis. Hypochondrogenesis is caused when type II collagen is abnormally formed due to a mutation in the COL2A1 gene; the cartilaginous notochord develops into the bony vertebrae in a human body.
The COL2A1 gene results in malformed type II collagen, essential in the transition from collagen to bone. This is the first time that researchers found a persistent notochord in a human body due to a COL2A